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Data · dataset · 2015

Ocular Neuromyotonia Associated with Chronic Inflammatory Demyelinating Polyneuropathy

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Ocular neuromyotonia (ONM) is a neuro-ophthalmic disorder characterized by episodic diplopia caused by contraction of one or more ocular muscles due to spontaneous excitation of the respective ocular motor nerve.

Description

We report a patient whose ocular neuromyotonia arose in the setting of a subacute demyelinating polyneuropathy consistent with chronic inflammatory demyelinating polyneuropathy (CIDP) and subsequently resolved following the initiation of intravenous immunoglobulin (IVIg) for her neuropathy.

Our patient provides additional evidence towards the role of demyelination and ephaptic neurotransmission in ocular neuromyotonia and also represents the first reported case of ocular neuromyotonia associated with a systemic neurological condition.

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Provenance · 1 source records, 11 field assertions
SourceKeyLast seenRaw
DataCite10.6084/m9.figshare.1568176.v112 d agoJSON v1
FieldAssertionExtractorEvidence
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concepts[field].fos:biological-sciencessource · DataCiteconnector:datacite@1.0.0
concepts[field].fos:clinical-medicinesource · DataCiteconnector:datacite@1.0.0
concepts[field].local:field:life-sciencesmapping · DataCitevocabulary-mapper@1.0.0keywords['Biological Sciences']
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publication_datesource · DataCiteconnector:datacite@1.0.0/data/attributes/dates
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