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Table · dataset · 2026

Supplemental Material for: Primary Perianal Paget’s Disease Treated by Bilateral Lotus Petal Flaps: A Case Report

Listed in ZivaHub and Deakin Research Online and DMU Figshare and HKU DataHub and Swinburne Figshare and DaYta Ya Rona and SUNScholarData and figshare and Loughborough Research Repository and GRANTS Data and UP Research Data Repository — shown once because both records carry DOI 10.6084/m9.figshare.34042803.v1

<p dir="ltr">Introduction: Perianal Paget’s disease (PPD) is a rare intraepidermal adenocarcinoma with frequent diagnostic delay and a high risk of local recurrence.

Description

When disease is confined to the epidermis, wide local excision with negative margins is preferred; reconstruction must balance infection risk, anal function, and cosmesis.</p><p><br></p><p dir="ltr">Case presentation: A 55-year-old woman presented with a well-demarcated, pruritic perianal plaque.

Biopsies identified Paget cells. Immunohistochemistry supported primary extramammary Paget’s disease. Comprehensive staging showed no associated malignancy.

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After multidisciplinary review, fecal diversion with laparoscopic sigmoid colostomy preceded wide local excision with an intended 1-cm margin. Reconstruction used bilateral lotus petal fasciocutaneous flaps based on internal pudendal vessel perforators, elevated in the subfascial plane and rotated to resurface the defect; donor sites were closed primarily. Pathology confirmed extramammary Paget’s disease with negative margins.

Recovery was uneventful. At 6-month surveillance, the reconstruction was tension-free with no complications or clinical/imaging evidence of recurrence.</p><p><br></p><p dir="ltr">Conclusion: Primary perianal Paget’s disease may present with nonspecific symptoms, making histopathological confirmation essential. Surgical excision remains the mainstay of treatment due to high recurrence rates, while reconstruction is challenging because of anatomical and functional constraints.

In this context, the lotus petal flap provides a reliable reconstructive option, offering adequate vascularity, functional preservation, and acceptable cosmetic outcomes following wide local excision. This case illustrates that a staged, multidisciplinary approach combining oncologically sound resection with bilateral lotus petal flap reconstruction can provide durable coverage and satisfactory functional and aesthetic results, particularly for large perianal defects when diversion is warranted.

Rigorous exclusion of synchronous malignancy and long-term surveillance remain essential.</p>

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Where it is published

Catalogue records · 1

Topics

Inferred from text
Disease 75% · Imaging 75%
Provenance · 11 source records, 56 field assertions
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ZivaHuboai:figshare.com:article/3404280312 d agoJSON v1
Deakin Research Onlineoai:figshare.com:article/3404280312 d agoJSON v1
DMU Figshareoai:figshare.com:article/3404280312 d agoJSON v1
HKU DataHuboai:figshare.com:article/3404280312 d agoJSON v1
Swinburne Figshareoai:figshare.com:article/3404280312 d agoJSON v1
DaYta Ya Ronaoai:figshare.com:article/3404280312 d agoJSON v1
SUNScholarDataoai:figshare.com:article/3404280312 d agoJSON v1
figshareoai:figshare.com:article/3404280312 d agoJSON v1
Loughborough Research Repositoryoai:figshare.com:article/3404280311 d agoJSON v1
GRANTS Dataoai:figshare.com:article/3404280311 d agoJSON v1
UP Research Data Repositoryoai:figshare.com:article/3404280311 d agoJSON v1
FieldAssertionExtractorEvidence
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