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Table · dataset · 2026

Supplemental Material for: Localized intestinal amyloidosis case report – uncommon presentation of a rare disease

Listed in figshare and Loughborough Research Repository — shown once because both records carry DOI 10.6084/m9.figshare.33963091.v1

<p dir="ltr">Introduction: Amyloidosis involves a heterogeneous group of diseases resulting from extracellular deposition of abnormal fibrillar proteins.

Description

Systemic and localized forms of the disease are recognized, with distinct presentations and prognoses.</p><p dir="ltr">Case presentation: We report the case of a 70-year-old male with a history of diarrhoea and weight loss. Upper gastrointestinal endoscopy revealed duodenal mucosal thickening and whitish granularity.

Biopsies showed a positive Congo Red staining. Aetiological investigation was negative. Thus, localized intestinal amyloidosis was diagnosed.

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The patient was medicated with rifaximin and loperamide for symptomatic control.</p><p dir="ltr">Discussion/conclusion: Gastrointestinal tract involvement in systemic amyloidosis carries a worse prognosis. Localized amyloidosis is a rarer variant of the disease, with better prognosis and no known cases of progression. Follow-up consists of symptomatic control.

This highlights a rare form of amyloidosis with benign clinical course, in which invasive or aggressive treatments should be avoided.</p>

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Inferred from text
Disease 75%
Provenance · 2 source records, 29 field assertions
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